Article Type
Case Report
Abstract
Background: Portal vein thrombosis (PVT) is a serious complication that may occur post-splenectomy in patients with β -thalassemia intermedia. This complication is particularly prevalent among individuals with iron overload and protein C and S deficiencies. Diagnostic investigations for PVT include blood tests and imaging assessments, such as abdominal Doppler ultrasound and computed tomography (CT). Advanced imaging techniques are crucial for the diagnosis and management of PVT, with improved outcomes associated with early anticoagulant therapy. Surgical thrombectomy is rarely recommended in such cases. The prognosis for PVT in patients who are not cirrhotic and do not have cancer is favorable, with an average survival rate of 92% after one year and 76% after five years. Case Presentation: A 15-year-old female diagnosed with β -thalassemia intermedia, who had received occasional blood transfusions, underwent splenectomy at the age of 7. She was admitted to the hematology ward due to insidious onset and progressive abdominal pain lasting over 10 days. Investigations confirmed the diagnosis of acute PVT. Conclusion: This case involved a young female with protein C and S deficiencies, thalassemia intermedia, and a history of splenectomy, all of which are common risk factors for PVT. Advanced imaging techniques are increasingly important for the diagnosis and management of PVT, with improved outcomes associated with early anticoagulant therapy.
Keywords
Portal vein thrombosis, β -thalassemia intermedia, Iraq
Recommended Citation
Jaber, Rawshan Zuhair
(2026)
"Acute Portal Vein Thrombosis in β -Thalassemia Intermedia: A Case Report,"
Iraqi National Journal of Medicine: Vol. 8
:
Iss.
2
, Article 5.
Available at:
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